Van Bogaert-Scherer-Epstein Syndrome: A Comprehensive Review of a Rare Neurological Disorder
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Abstract
The Van Bogaert-Scherer-Epstein Syndrome (VBSES), also known as Van Bogaert-Scherer-Epstein Disease, is an exceedingly rare and enigmatic neurologic disorder characterized by a complex constellation of clinical symptoms and radiographic findings. Despite its scarcity, VBSES has been a subject of intrigue for medical professionals and researchers due to its intriguing pathogenesis and the challenges it presents in diagnosis and management. In this article, we aim to provide an extensive overview of VBSES, encompassing its historical context, clinical manifestations, diagnostic criteria, radiological features, pathophysiological mechanisms, and therapeutic interventions. Drawing upon an extensive review of the existing literature and a synthesis of relevant case studies, we offer an in-depth analysis of VBSES, shedding light on the current state of knowledge and highlighting the importance of continued research in unraveling this perplexing neurological syndrome
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