Periprosthetic Femur Fracture on Alkaptonuric Patient: A Rare Case Report in Indonesia

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Published: Mar 30, 2023
DOI: https://doi.org/10.47191/ijmscrs/v3-i3-44
Keywords:
alkaptonuria periprosthetic fracture total knee arthroplasty ochronosis MIPO

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Nyoman Gede Grenata Nanda Ustriyana
Resident Medical Officer, Siloam Hospital Denpasar, Bali, Indonesia.
Putu Dewinta Darmada
Resident Medical Officer, Siloam Hospital Denpasar, Bali, Indonesia.
Hasnania Rilanty Munaf
Global Health/Health Leadership and Management, University of New South Wales, Sydney, Australia.
Erwin Saspraditya
Department of Orthopaedic and Traumatology Surgery, Siloam Hospital Denpasar, Bali, Indonesia.
Putu Budi Sucitra
Department of Orthopaedic and Traumatology Surgery, Siloam Hospital Denpasar, Bali, Indonesia.

Abstract

A 74-year-old male with alkaptonuria (AKU) was admitted to the emergency department with left distal femur pain and Rorabeck type 2 periprosthetic femur fracture following total knee arthroplasty (TKA). AKU is an autosomal recessive disorder characterized by homogentisic acid buildup in connective tissues and joints, leading to ochronosis and arthritis. Multiple joint replacements are common in AKU patients, and periprosthetic fractures may occur due to osteopenia. Rorabeck type 2 fracture is treated with intramedullary nailing or locked plating. The patient underwent internal fixation with locking plate and bone grafts using minimally invasive plate osteosynthesis (MIPO) procedure, resulting in good fracture healing. The case highlights the importance of considering AKU as a differential diagnosis in arthritis patients and managing periprosthetic fractures with care in AKU patients.

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How to Cite
Ustriyana, N. G. G. N., Darmada, P. D., Munaf, H. R., Saspraditya, E., & Sucitra, P. B. (2023). Periprosthetic Femur Fracture on Alkaptonuric Patient: A Rare Case Report in Indonesia. International Journal of Medical Science and Clinical Research Studies, 3(3), 570–575. https://doi.org/10.47191/ijmscrs/v3-i3-44
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Vol. 3 No. 3 (2023): Volume 03 Issue 03 March 2023
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Articles
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This work is licensed under a Creative Commons Attribution 4.0 International License.

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