Vulvo-Perineal Crohn’s Disease: A Challenging Diagnosis!

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Published: Aug 5, 2024
DOI: https://doi.org/10.47191/ijmscrs/v4-i08-02
Keywords:
Vulvo-perineal- Crohn’s disease- knife-shaped ulcerations- non-caseating granuloma.

Main Article Content

Hali Fouzia
Department of Dermatology and Venereology, Ibn Rochd University hospital, Hassan II University, Casablanca
Zakaryaa Salma
Department of Dermatology and Venereology, Ibn Rochd University hospital, Hassan II University, Casablanca
Baghad Bouchra
Department of Dermatology and Venereology, Ibn Rochd University hospital, Hassan II University, Casablanca
Marnissi Farida
Anatomopathology Department, Ibn Rochd University hospital, Hassan II University, Casablanca
Hliwa Wafaa
Gastrology department, Ibn Rochd University hospital, Hassan II University, Casablanca
Chiheb Soumiya
Department of Dermatology and Venereology, Ibn Rochd University hospital, Hassan II University, Casablanca

Abstract

Crohn's disease (CD) is a chronic inflammatory bowel disease with polymorphous cutaneous manifestations. Vulvar localization is rare and may be either isolated, revealing the disease, or associated with digestive manifestations. Treatment is difficult and not well codified.


Based on 4 case reports of vulvo-perineal involvement, we present a reminder of the diagnostic and therapeutic challenges of this particular site.


In 2 out of 4 patients, vulvar involvement was incipient, with no gastrointestinal symptoms at the time of diagnosis. The vulva may present with many dermatological manifestations: knife-like ulcerations, oedema, labial hypertrophy, lymphangiectasia, abscesses and fistulae. The presence of non-caseating granulomas on histology may help to confirm the diagnosis.


Vulvar CD affects quality of life and requires long-term medical and surgical management with a multidisciplinary approach involving gastroenterologists, dermatologists, gynecologists and pathologists.

Article Details

How to Cite
Hali Fouzia, Zakaryaa Salma, Bouchra, B., Farida, M., Hliwa Wafaa, & Chiheb Soumiya. (2024). Vulvo-Perineal Crohn’s Disease: A Challenging Diagnosis!. International Journal of Medical Science and Clinical Research Studies, 4(08), 1437–1440. https://doi.org/10.47191/ijmscrs/v4-i08-02
Issue
Vol. 4 No. 08 (2024): Volume 04 Issue 08 August 2024
Section
Articles
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This work is licensed under a Creative Commons Attribution 4.0 International License.

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